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In-vitro and in-vivo consequences of mutations in the von Willebrand factor cleaving protease ADAMTS 13 in thrombotic thrombocytopenic purpura
| Content Provider | Semantic Scholar |
|---|---|
| Author | Donadelli, Roberta Banterla, Federica Galbusera, Miriam Capoferri, Cristina Bucchioni, Sara Gastoldi, Sara Nosari, Silvia Monteferrante, Giuseppe Ruggeri, Zaverio M. Bresin, Elena Scheiflinger, Friedrich Martínez, Constantino Coppo, Rosanna Remuzzi, Giuseppe Noris, Marina |
| Copyright Year | 2018 |
| Abstract | Roberta Donadelli1, Federica Banterla1, Miriam Galbusera1, Cristina Capoferri1, Sara Bucchioni2, Sara Gastoldi1, Silvia Nosari2, Giuseppe Monteferrante2, Zaverio M. Ruggeri3, Elena Bresin2, Friedrich Scheiflinger4, Edoardo Rossi5, Constantino Martinez6, Rosanna Coppo7, Giuseppe Remuzzi1,8, Marina Noris2; on behalf of the International Registry of Recurrent and Familial HUS/TTP 1Mario Negri Institute for Pharmacological Research, Bergamo, Italy; 2Clinical Research Center for Rare Diseases, Aldo e Cele Daccò,Villa Camozzi-Ranica, Italy; 3Roon Center for Arteriosclerosis and Thrombosis, Division of Experimental Hemostasis and Thrombosis, Department of Molecular and Experimental Medicine, The Scripps Research Institute, La Jolla, California, USA; 4Baxter BioScience, Biomedical Research Center, Orth/Donau, Austria; 5Immunohematology and Blood Transfusion Service, Luigi Sacco Hospital, Milan, Italy ; 6Centro Regional de Hemo-donación, University of Murcia, Spain; Department of Nephrology, Dialysis and Transplantatiuon, Regina Margherita Hospital, Turin, Italy; 8Division of Nephrology and Dialysis, Azienda Ospedaliera, Ospedali Riuniti di Bergamo, Bergamo, Italy |
| File Format | PDF HTM / HTML |
| Alternate Webpage(s) | https://th.schattauer.de/en/contents/archive/issue/755/manuscript/7244/download.html |
| Language | English |
| Access Restriction | Open |
| Content Type | Text |
| Resource Type | Article |