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Cardiopatia e desenvolvimento motor na Síndrome de Down: série de casos
| Content Provider | Semantic Scholar |
|---|---|
| Author | Hoepers, Andreza Schenkel, Isabel De Castro Schivinski, Camila Isabel Santos |
| Copyright Year | 2013 |
| Abstract | Considerada a sindrome mais comum na populacao, a sindrome de Down (SD) e caracterizada por atrasos motores decorrentes da hipotonia muscular generalizada e frouxidao ligamentar. Malformacoes podem estar associadas, mas sao as cardiopatias congenitas (CC) que influenciam diretamente no prognostico, principalmente no primeiro ano de vida. Sendo assim, o objetivo desse relato de uma serie de casos foi de apresentar o desenvolvimento motor de criancas com SD, portadoras e nao portadoras de CC. Alem disso, comparar os resultados com marcos de desenvolvimento ja descritos na literatura e relacionar com aspectos socio-economicos. Para isso, participaram 8 criancas, com media de idade de 13,72 meses, sendo 5 sem CC e 3 cardiopatas. As criancas foram submetidas a aplicacao da escala Brunet e Lezine para a avaliacao do desenvolvimento motor e os pais responderam um questionario referente a dados socio-economicos e condicoes pre, peri e pos-natal. As criancas sem CC apresentaram classificacao muito inferior ou inferior, em quase todas as areas da escala, com excecao de dois casos, que tiveram um desempenho um pouco melhor nas areas postural, social, oculomotriz e global. Um destes casos apresentou nivel normal baixo na area da linguagem e social. No grupo de cardiopatas, um dos casos nao apresentou nenhum resultado abaixo de normal medio e uma crianca demonstrou um nivel acima do muito inferior apenas no item social. Esta serie de casos identificou criancas com SD cardiopatas com desenvolvimento motor semelhante ao de criancas sem CC, sendo que fatores socio- economicos podem ter influenciado neste resultado Considered the most common syndrome in the population, Down syndrome (DS) is characterized by motor delays arising from generalized muscle hypotonia and ligament laxity. Malformations may be associated with the syndrome, but congenital heart disease (CHD) are directly influencing the prognosis of patients, especially in the first year of life. Therefore, the purpose of this report a case series was to present the evaluation of motor development in children with DS, suffering and not suffering with CHD. Moreover, comparing the results with developmental milestones already described in the literature and relate to socio-economic aspects. The participants were 8 children, mean age was 13.72 months, and 5 patients without CHD and 3 heart disease. Children were submitted to the scale and Brunet Lezine for the assessment of motor development and the parents answered a questionnaire on the socio-economic conditions and prenatal, perinatal and postnatal periods. Children without CHD had much lower ratings, or less, in almost all areas, except for two cases where, who fared a little better in the areas posture, social, and global oculomotriz. One of these cases had low normal level in the area of language and social. In the group of CHD children, a case has not produced any result below the normal average and one child showed a much lower level above only in the social item. This series of cases identified CHD children with motor development similar to that of DS without CHD, and socioeconomic factors may have influenced this result. |
| Starting Page | 86 |
| Ending Page | 92 |
| Page Count | 7 |
| File Format | PDF HTM / HTML |
| Volume Number | 42 |
| Alternate Webpage(s) | http://www.acm.org.br/revista/pdf/artigos/1234.pdf |
| Language | English |
| Access Restriction | Open |
| Content Type | Text |
| Resource Type | Article |