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Pulmonary congenital cystic adenomatoid malformation, type I, presenting as a single cyst of the middle lobe in an adult: case report
| Content Provider | Semantic Scholar |
|---|---|
| Author | Morelli, Luca Piscioli, Irene Licci, Stefano Donato, Salvatore Catalucci, Alessia Nonno, Franca Del |
| Copyright Year | 2007 |
| Abstract | BACKGROUND Congenital cystic adenomatoid malformation (CCAM) of the lung is an uncommon fetal development anomaly of the terminal respiratory structures. The large cyst type usually occurs in stillborn infants or newborn infants with respiratory distress. Cases of CCAM have been previously described in adulthood, more often type I with multiloculated cystic lesions. CASE PRESENTATION We report a case of type I CCAM presenting as a single, expansive cystic mass in the middle pulmonary lobe in a 38-year-old man, revealed by persistent cough and haemoptysis. Computed tomographic scan showed a single cyst with air fluid level, occupying the lateral segment of the lobe. When the type I CCAM is a single cyst, other cystic pulmonary lesions must be excluded. The intrapulmonary localization and the absence of cartilage in the cyst wall are conclusive findings of CCAM. The pathogenesis, management and differential diagnosis with other lung malformations are discussed along with a review of the literature. CONCLUSION The literature data confirm that surgical resection is the treatment of choice in all cases of CCAM and in the cases of cystic pulmonary lesions with uncertain radiological findings, in order to perform a histological examination of the lesion and to prevent infection and the potential neoplastic transformation. |
| Starting Page | 17 |
| Ending Page | 17 |
| Page Count | 1 |
| File Format | PDF HTM / HTML |
| PubMed reference number | 17555585v1 |
| Volume Number | 2 |
| Journal | Diagnostic pathology |
| Alternate Webpage(s) | http://download-redirector.springer.com/redirect?contentType=pdf&ddsId=art:10.1186/1746-1596-2-17&originUrl=http://diagnosticpathology.biomedcentral.com/article/10.1186/1746-1596-2-17 |
| Language | English |
| Access Restriction | Open |
| Subject Keyword | Cartilage Congenital Abnormality Congenital Cystic Adenomatoid Malformation, Type I Coughing Cystic Adenomatoid Malformation of Lung, Congenital Cystic Kidney Diseases Excision Exclusion Fetal development of the mammalian embryo or fetus Hemoptysis Idiopathic Pulmonary Fibrosis Infant, Newborn Lung diseases Neoplastic Cell Transformation Pulmonary Valve Insufficiency Respiratory Distress Syndrome, Newborn Structure of lobe of lung Structure of middle lobe of right lung Structure of parenchyma of lung cyst wall |
| Content Type | Text |
| Resource Type | Article |
