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Intestinal neurofibromatosis and small-bowel adenocarcinoma: a single case study.
| Content Provider | Semantic Scholar |
|---|---|
| Author | Stratopoulos, Charalabos Papakonstantinou, Alexandros Anagnostopoulos, George T. Terzis, Ioannis Tzimas, George Gourgiotis, S. Tavros Vamvouka, Chrysanthi Hadjiyannakis, Evangelos I. |
| Copyright Year | 2009 |
| Abstract | OBJECTIVE Patients with Von Recklinghausen's disease (neurofibromatosis type 1) are at increased risk of developing various tumours. However, the coexistence of neurofibromatosis with small-bowel adenocarcinoma is exceedingly rare. We present an uncommon case of neurofibromatosis type 1, involving the small bowel in a 73-year-old man, who was admitted to our department with signs of acute abdomen. At laparotomy, multiple mesenteric and intramural nodules were seen in the distal ileum. These nodules obstructed ileal lumen, while the intestine wall was perforated in one point. A wide resection of the affected ileum together with all visible nodules in the adjacent mesentery was performed. Histology revealed neurofibromatosis type 1 with malignant transformation to small-bowel adenocarcinoma. The patient had no additional therapy. In a follow-up of 2 years, the patient is very well and there was no recurrence of the disease. We suggest that adenocarcinoma of small bowel should be considered in the evaluation of acute abdominal pain in neurofibromatosis patients. |
| Starting Page | 3 |
| Ending Page | 8 |
| Page Count | 6 |
| File Format | PDF HTM / HTML |
| Alternate Webpage(s) | http://www.stavrosgourgiotis.gr/wp-content/uploads/2015/04/Intestinal-neurofibromatosis-and-small-bowel-adenocarcinoma.pdf |
| PubMed reference number | 19473375v1 |
| Alternate Webpage(s) | https://doi.org/10.1111/j.1365-2354.2007.00888.x |
| DOI | 10.1111/j.1365-2354.2007.00888.x |
| Journal | European journal of cancer care |
| Volume Number | 18 |
| Issue Number | 5 |
| Language | English |
| Access Restriction | Open |
| Subject Keyword | Abdomen, Acute Abdominal Pain Adenocarcinoma of the small intestine Hospital admission Intestines Intestines, Small Laparotomy Malignant Childhood Central Nervous System Neoplasm Mesentery Neoplasms Neurofibromatoses Neurofibromatosis 1 Non-Small Cell Lung Carcinoma Paget's Disease, Mammary Patients Small Intestinal Wall Tissue Structure of lumen of body system |
| Content Type | Text |
| Resource Type | Article |
