Shone's anomaly: a report of one case in sub-Saharan Africa.

Content Provider	Europe PMC
Author	Nkoke, Clovis Lekoubou, Alain Yonta, Edvine Wawo Dzudie, Anastase Kengne, Andre Pascal
Copyright Year	2014
Abstract	Shone’s anomaly is a rare congenital cardiac malformation consisting of four obstructive lesions of the left heart and the aortic arch: a supramitral membrane; parachute mitral valve; subaortic stenosis; and coarctation of the aorta which occurs most commonly in its incomplete form. We report on a 17-year-old male Cameroonian with a variant of shone anomaly consisting of sub-valvular aortic stenosis, coarctation of the aorta and parachute mitral valve. He was referred for the investigation of a cardiac murmur after he presented with shortness of breath preceded by flu like syndrome. He underwent successful management abroad consisting of aortic coarctation treatment by percutaneous angioplasty and resection of the subaortic ring by traditional surgical approach without any mitral valve repair. Shone’s anomaly is a rare congenital heart disease that can be missed in low resource settings. This case raises awareness about this syndrome, highlights the importance of cardiac ultrasonography in resource limited settings and illustrates the need for comprehensive service frameworks to improve access and level of care and services for patients in the African context.
Related Links	https://europepmc.org/backend/ptpmcrender.fcgi?accid=PMC4278041&blobtype=pdf
ISSN	22233652
Volume Number	4
DOI	10.3978/j.issn.2223-3652.2014.12.04
PubMed Central reference number	PMC4278041
Issue Number	6
PubMed reference number	25610807
Journal	Cardiovascular Diagnosis and Therapy [Cardiovasc Diagn Ther]
e-ISSN	22233660
Language	English
Publisher	AME Publishing Company
Publisher Date	2014-12-01
Access Restriction	Open
Rights License	2014 Cardiovascular Diagnosis and Therapy. All rights reserved.
Subject Keyword	Congenital heart disease Shone’s anomaly Cameroon Sub-Saharan Africa (SSA)
Content Type	Text
Resource Type	Article
Subject	Cardiology and Cardiovascular Medicine